[{"data":1,"prerenderedAt":64},["ShallowReactive",2],{"q-nurse-114-2-maternal-pediatric-050":3},{"subject":4,"subjectSlug":5,"subjectFullName":4,"question":6,"related":33,"lastmod":63},"產兒科護理學","maternal-pediatric",{"id":7,"webId":8,"year":9,"session":10,"subject":4,"number":11,"stem":12,"options":13,"answer":18,"answerNote":19,"images":20,"explanation":21,"explanationDeep":22,"topics":23,"freq":10},"nurse-114-2-產兒科護理學-050","nurse-114-2-maternal-pediatric-050",114,2,50,"張小弟，9 歲，確診為裘馨氏假肥大性肌失養症（Duchenne’s pseudohy-pertrophic muscular dystrophy），有關護理指導，下列何者最不適當？",{"A":14,"B":15,"C":16,"D":17},"鼓勵家屬因應疾病發展彈性調整家中環境","鼓勵張小弟參與高密度游泳活動，以增強肌肉張力","每日為張小弟進行胸部物理治療，降低罹患肺炎的風險","進行飲食計畫，控制體重以減少負荷","B",null,[],"本題考點在於裘馨氏肌失養症的疾病進程與活動安全指導。此症為 X 染色體性聯隱性遺傳，dystrophin 缺乏使肌肉進行性退化，肌力隨年齡下降，過度或高強度運動不僅無法增強肌張力，反而加速肌肉損傷與疲乏。本題為反向題，最不適當者為 B：鼓勵高密度游泳「增強肌肉張力」是錯誤觀念，應改為溫和、不過度的活動維持關節活動度。A 適當，隨疾病進展彈性調整居家環境（如輪椅動線）符合漸進失能需求；C 適當，每日胸部物理治療可清除分泌物、降低呼吸肌無力導致的肺炎風險；D 適當，控制體重可減輕虛弱肌肉與心肺負荷。","機轉：DMD 因 dystrophin 基因缺陷，肌纖維反覆壞死並被脂肪纖維取代，出現假性肥大（尤其小腿）。典型 Gower's sign（以手撐大腿站起）。運動原則是「維持」而非「強化」，避免離心與高負荷運動造成肌損；後期死因多為呼吸衰竭與心肌病變，故胸部物理治療與體重控制是重點。",[24,26,29,31],{"term":25,"count":10},"裘馨氏肌失養症",{"term":27,"count":28},"dystrophin 缺乏",1,{"term":30,"count":28},"假性肥大",{"term":32,"count":28},"運動安全與胸部物理治療",[34,38,43,48,53,58],{"webId":35,"stem":36,"number":28,"year":9,"session":37},"nurse-114-3-maternal-pediatric-001","有關因應少子化的相關政策，下列敘述何者最不適當？",3,{"webId":39,"stem":40,"number":41,"year":42,"session":28},"nurse-115-1-maternal-pediatric-047","王小弟，8 個月，罹患先天性膽道閉鎖，手術後偶有膽道炎發生，有關飲食護理指導的敘述，下列何者正確？",47,115,{"webId":44,"stem":45,"number":46,"year":47,"session":28},"nurse-106-1-maternal-pediatric-041","下列何者不是 16 歲青少女神經性厭食症的表徵？",41,106,{"webId":49,"stem":50,"number":51,"year":52,"session":28},"nurse-107-1-maternal-pediatric-079","王小弟，4 週大，因幽門狹窄（pyloric stenosis）接受幽門切開術（pyloromyotomy）。下列有關護理措施之敘述，何者錯誤？",79,107,{"webId":54,"stem":55,"number":56,"year":57,"session":10},"nurse-108-2-maternal-pediatric-043","依據常見的嬰幼兒發展現象，一般嬰幼兒乳齒的生長順序，下列何者正確？①上排中央門牙 ②下排中央門牙 ③犬齒 ④第一臼齒 ⑤第二臼齒",43,108,{"webId":59,"stem":60,"number":61,"year":62,"session":10},"nurse-109-2-maternal-pediatric-077","有關提供癲癇病童長期服用抗癲癇藥物的護理措施，下列何者錯誤？",77,109,"2026-09-04",1788510760375]