[{"data":1,"prerenderedAt":66},["ShallowReactive",2],{"q-nurse-114-2-maternal-pediatric-043":3},{"subject":4,"subjectSlug":5,"subjectFullName":4,"question":6,"related":35,"lastmod":65},"產兒科護理學","maternal-pediatric",{"id":7,"webId":8,"year":9,"session":10,"subject":4,"number":11,"stem":12,"options":13,"answer":18,"answerNote":19,"images":20,"explanation":21,"explanationDeep":22,"topics":23,"freq":26},"nurse-114-2-產兒科護理學-043","nurse-114-2-maternal-pediatric-043",114,2,43,"潘小弟，3 歲，因為身體不適至醫院求治，經醫師診斷後確診為血友病，有關臨床表徵的敘述，下列何者正確？",{"A":14,"B":15,"C":16,"D":17},"皮膚出現瘀血，刷牙時牙齦出血","臉色蒼白，呼吸快速或突然昏倒","易疲倦、食慾不振，身體易感染","皮膚出現黃疸現象，肝、脾腫大","A",null,[],"本題考點在於血友病的出血型臨床表徵。依病生理，血友病為凝血因子缺乏(A型缺第VIII因子、B型缺第IX因子)導致凝血功能異常，表現為皮膚瘀血、刷牙牙齦出血與關節腔出血等，故選A。B臉色蒼白、突然昏倒偏向急性失血或休克；C易疲倦、食慾不振、易感染較像白血病或再生不良性貧血；D黃疸與肝脾腫大屬溶血或肝膽問題，皆非血友病典型表現。","血友病為X染色體隱性遺傳,多見於男性。特徵是次發性凝血異常:凝血酶原時間正常、部分凝血活酶時間(aPTT)延長。反覆關節腔出血(血關節)可致關節變形是長期併發症。護理:避免肌肉注射與阿斯匹靈、防跌防外傷、必要時補充凝血因子。",[24,27,30,33],{"term":25,"count":26},"血友病",6,{"term":28,"count":29},"凝血因子缺乏",3,{"term":31,"count":32},"關節腔出血",1,{"term":34,"count":32},"aPTT延長",[36,40,45,50,55,60],{"webId":37,"stem":38,"number":39,"year":9,"session":10},"nurse-114-2-maternal-pediatric-044","劉小妹， 3 歲，罹患急性淋巴性白血病，經過血液常規檢查發現，白血球： 2,500\u002Fmm 3 ，多型核白血球（segment）： 8%，帶狀白血球（band）：10%，其絕對嗜中性白血球（absolut neutrophil count, ANC）是多少？",44,{"webId":41,"stem":42,"number":43,"year":44,"session":32},"nurse-115-1-maternal-pediatric-040","安撫躁動不安的法洛氏四重畸形病童，經常採取膝胸臥式或蹲姿，有關彎曲腿部的理由，下列敘述何者錯誤？",40,115,{"webId":46,"stem":47,"number":48,"year":49,"session":32},"nurse-106-1-maternal-pediatric-034","形成妊娠中期心灼熱感（heart burn）的荷爾蒙為下列何者？",34,106,{"webId":51,"stem":52,"number":53,"year":54,"session":32},"nurse-107-1-maternal-pediatric-072","先天性心臟病的嬰兒常因餵食困難而造成營養攝取不足。有關嬰兒餵食的護理措施，下列敘述何者錯誤？",72,107,{"webId":56,"stem":57,"number":58,"year":59,"session":10},"nurse-108-2-maternal-pediatric-036","有關心臟病婦女妊娠期護理之敘述，下列何者錯誤？",36,108,{"webId":61,"stem":62,"number":63,"year":64,"session":10},"nurse-109-2-maternal-pediatric-070","小美 5 歲，出現發燒、臉色蒼白、虛弱、肚子痛，經醫師確診為神經母細胞瘤第三期，下列敘述何者最不適當？",70,109,"2026-09-04",1788510760296]