[{"data":1,"prerenderedAt":67},["ShallowReactive",2],{"q-nurse-114-1-maternal-pediatric-042":3},{"subject":4,"subjectSlug":5,"subjectFullName":4,"question":6,"related":35,"lastmod":66},"產兒科護理學","maternal-pediatric",{"id":7,"webId":8,"year":9,"session":10,"subject":4,"number":11,"stem":12,"options":13,"answer":18,"answerNote":19,"images":20,"explanation":21,"explanationDeep":22,"topics":23,"freq":26},"nurse-114-1-產兒科護理學-042","nurse-114-1-maternal-pediatric-042",114,1,42,"有關苯酮尿症（phenylketonuria）之護理指導，下列何者錯誤？",{"A":14,"B":15,"C":16,"D":17},"為體染色體隱性遺傳的疾病，會遺傳給下一代","禁餵母奶，須餵食低苯胺基丙酸（如：lofenalac）或不含苯丙胺酸（如：phenyl-free）之配方奶","飲食須富含蛋白質食物，避免產生神經系統後遺症","不治療會有髮色淡黃、霉臭味尿液、智力不足症狀","C",null,[],"本題考點在於苯酮尿症（PKU）的飲食與遺傳護理指導。本題為反向題，錯誤敘述為 C：PKU 因苯丙胺酸羥化酶缺乏，無法代謝苯丙胺酸（phenylalanine），飲食須「限制」高蛋白食物（蛋白質富含苯丙胺酸），而非富含蛋白質，故 C 錯誤。A 屬體染色體隱性遺傳，會傳給下一代，正確。B 母奶含苯丙胺酸須禁餵，改用低或不含苯丙胺酸配方（如 Lofenalac、Phenyl-free），正確。D 未治療會出現髮色淡、尿液霉臭味與智力障礙，正確。","PKU 為體染色體隱性代謝疾病，苯丙胺酸堆積產生苯酮酸經尿排出（霉\u002F鼠臭味），並沉積傷腦致智能不足；黑色素合成受阻故膚髮偏淡。治療核心是終生限苯丙胺酸飲食，同時須供給足夠替代蛋白維持生長。新生兒篩檢（足跟採血）是早期偵測關鍵，及早飲食控制可預防不可逆腦損傷。",[24,27,30,33],{"term":25,"count":26},"新生兒篩檢",13,{"term":28,"count":29},"體染色體隱性遺傳",11,{"term":31,"count":32},"苯酮尿症",4,{"term":34,"count":10},"苯丙胺酸限制",[36,40,45,51,56,61],{"webId":37,"stem":38,"number":39,"year":9,"session":10},"nurse-114-1-maternal-pediatric-043","有關初診斷白血病的臨床表徵，下列敘述何者最適當？",43,{"webId":41,"stem":42,"number":43,"year":9,"session":44},"nurse-114-3-maternal-pediatric-039","小玉，2 歲，因感冒罹患急性中耳炎（acute otitis media）住院治療，其返家之護理照護，下列敘述何者正確？",39,3,{"webId":46,"stem":47,"number":48,"year":49,"session":50},"nurse-115-2-maternal-pediatric-033","評估嬰兒術後疼痛，下列量表何者最適宜？",33,115,2,{"webId":52,"stem":53,"number":54,"year":55,"session":10},"nurse-107-1-maternal-pediatric-021","楊女士剖腹產後第二天開始進食，主訴腹脹不舒服，下列措施何者不恰當？",21,107,{"webId":57,"stem":58,"number":59,"year":60,"session":10},"nurse-108-1-maternal-pediatric-065","有關囊性纖維變性（Cystic Fibrosis）之敘述，下列何者錯誤？",65,108,{"webId":62,"stem":63,"number":64,"year":65,"session":50},"nurse-109-2-maternal-pediatric-019","陰道生產的產後第二天，評估子宮底呈堅硬狀，位置在肚臍以下 2 公分，惡露呈紅色且小量，此時最適當的護理指導為何？",19,109,"2026-09-04",1788510758014]