[{"data":1,"prerenderedAt":64},["ShallowReactive",2],{"q-nurse-112-2-maternal-pediatric-077":3},{"subject":4,"subjectSlug":5,"subjectFullName":4,"question":6,"related":33,"lastmod":63},"產兒科護理學","maternal-pediatric",{"id":7,"webId":8,"year":9,"session":10,"subject":4,"number":11,"stem":12,"options":13,"answer":18,"answerNote":19,"images":20,"explanation":21,"explanationDeep":22,"topics":23,"freq":26},"nurse-112-2-產兒科護理學-077","nurse-112-2-maternal-pediatric-077",112,2,77,"有關肌肉失養症（Muscular Dystrophy）病童之臨床表徵與處置，下列敘述何者不適當？",{"A":14,"B":15,"C":16,"D":17},"症狀乃因缺乏肌縮蛋白（Dystrophin）導致","病童站立時出現巴羅氏徵象（Barlow’s sign）","游泳是促進全身肌肉強度最好的運動","血液檢查 CPK、aldolase、AST 數值偏高","B",null,[],"本題考點是肌肉失養症的臨床表徵，屬反向題。錯誤敘述為 B，巴羅氏徵象(Barlow's sign)是新生兒髖關節發育不良(DDH)的評估手法，與肌肉失養症無關；裘馨型肌肉失養症的典型表現是高爾氏徵象(Gower's sign)，即病童須用手撐著大腿逐步爬起，故選 B。裘馨型肌肉失養症因 X 染色體基因缺陷導致缺乏肌縮蛋白(Dystrophin)，A 正確。因肌纖維無力，低衝擊的游泳確能維持肌力且保護關節，C 正確。肌肉持續破壞使 CPK、aldolase、AST 等肌肉酵素升高，D 正確。","裘馨型肌肉失養症(DMD)為 X 性聯隱性遺傳，好發於男童，因 dystrophin 蛋白缺失使肌膜易受損。Gower's sign 是招牌考點，反映近端(骨盆帶)肌無力。假性肥大(小腿因脂肪與結締組織取代肌肉而變粗)也常考。對比記憶：Barlow\u002FOrtolani 徵象查髖關節脫位、Gower 徵象查近端肌無力，兩者常被出題者交換選項設陷阱。肌酸激酶(CPK)是早期敏感指標，可在症狀明顯前即升高。",[24,27,29,31],{"term":25,"count":26},"肌肉失養症 肌縮蛋白 Dystrophin",1,{"term":28,"count":26},"高爾氏徵象 Gower's sign",{"term":30,"count":26},"巴羅氏徵象 髖關節發育不良",{"term":32,"count":26},"CPK 肌肉酵素上升",[34,38,43,48,53,58],{"webId":35,"stem":36,"number":37,"year":9,"session":10},"nurse-112-2-maternal-pediatric-078","兒童罹患雷氏症候群（Reye’s Syndrome）常會有複雜性合併症產生，有關其病因和症狀，下列敘述何者正確？",78,{"webId":39,"stem":40,"number":41,"year":42,"session":26},"nurse-113-1-maternal-pediatric-044","有關性早熟（precocious puberty）的敘述，下列何者正確？",44,113,{"webId":44,"stem":45,"number":46,"year":42,"session":47},"nurse-113-3-maternal-pediatric-038","有關病童接受氧氣治療的照護措施，下列敘述何者最適當？",38,3,{"webId":49,"stem":50,"number":51,"year":52,"session":26},"nurse-115-1-maternal-pediatric-036","瀕死兒童出現肌肉緊張力降低，下列敘述何者最不適當？",36,115,{"webId":54,"stem":55,"number":56,"year":57,"session":10},"nurse-106-2-maternal-pediatric-060","小明，3 歲，發燒 38.5℃，哭鬧不安，胃口不好，活動力差，至小兒急診求治，診斷為急性鼻咽炎，有關小明的照護措施，何者較不適當？",60,106,{"webId":59,"stem":60,"number":61,"year":62,"session":26},"nurse-108-1-maternal-pediatric-014","胡女士子宮頸口全開，護理師協助產婦躺上產檯並準備生產，下列護理措施何者不合適？",14,108,"2026-09-04",1788510748653]