[{"data":1,"prerenderedAt":63},["ShallowReactive",2],{"q-nurse-112-1-maternal-pediatric-067":3},{"subject":4,"subjectSlug":5,"subjectFullName":4,"question":6,"related":33,"lastmod":62},"產兒科護理學","maternal-pediatric",{"id":7,"webId":8,"year":9,"session":10,"subject":4,"number":11,"stem":12,"options":13,"answer":18,"answerNote":19,"images":20,"explanation":21,"explanationDeep":22,"topics":23,"freq":26},"nurse-112-1-產兒科護理學-067","nurse-112-1-maternal-pediatric-067",112,1,67,"小美，17 歲女性，為 A 型血友病帶因者，到院做遺傳諮詢，下列敘述何者最適當？",{"A":14,"B":15,"C":16,"D":17},"告知若配偶基因正常，未來每一胎生男嬰有 1\u002F2 機率為血友病者","告知若配偶基因正常，則不會生下血友病的孩子","告知若配偶基因正常，未來生的男嬰不會發生血友病，女嬰則有機率是帶因者","告知若配偶基因正常，未來若生女嬰皆為帶因者但不會發病","A",null,[],"本題考點為 A 型血友病的 X 染色體隱性遺傳諮詢。母親為帶因者、父親基因正常時，其兒子各有 1\u002F2 機率遺傳到帶病 X 而發病、女兒各有 1\u002F2 機率為帶因者。正解 A 正確描述「男嬰有 1\u002F2 機率為血友病者」。B 錯，仍有患病男嬰可能；C 錯，男嬰有機會發病而非皆不發病；D 錯，女嬰只有 1\u002F2 為帶因者而非全部，故選 A。","血友病 A（第八凝血因子缺乏）為 X 染色體隱性遺傳。帶因母（XᴴX）×正常父（XY）：兒子 XᴴY（患病）或 XY（正常）各半；女兒 XᴴX（帶因）或 XX（正常）各半，女兒因有一正常 X 通常不發病。記憶：帶因母→兒子 1\u002F2 病、女兒 1\u002F2 帶因。溯源需區分帶因（carrier）與發病（affected）。",[24,27,29,31],{"term":25,"count":26},"A 型血友病",2,{"term":28,"count":26},"X 染色體隱性遺傳",{"term":30,"count":10},"帶因者遺傳機率",{"term":32,"count":10},"第八凝血因子",[34,38,43,48,53,58],{"webId":35,"stem":36,"number":37,"year":9,"session":10},"nurse-112-1-maternal-pediatric-068","小華，3 歲，在一週前發燒後身上突然出現多處紫斑，經醫師診斷為特發性血小板（Idiopathic Thrombocytopenic Purpura, ITP），下列敘述何者錯誤？",68,{"webId":39,"stem":40,"number":41,"year":9,"session":42},"nurse-112-3-maternal-pediatric-004","王女士主訴：「我懷孕後都不吃冰了，因擔心對孩子氣管不好」，下列護理師反應何者最適當？",4,3,{"webId":44,"stem":45,"number":46,"year":47,"session":10},"nurse-113-1-maternal-pediatric-048","有關兒童腦神經疾病導致的顱內壓升高（IICP），若無適切介入措施，常會造成兒童生命危險，下列護理措施何者正確？",48,113,{"webId":49,"stem":50,"number":51,"year":52,"session":26},"nurse-114-2-maternal-pediatric-046","有關新生兒先天性甲狀腺功能低下症（congenital hypothyroidism）的敘述，下列何者錯誤？",46,114,{"webId":54,"stem":55,"number":56,"year":57,"session":10},"nurse-106-1-maternal-pediatric-050","小強，15 個月大，被診斷有輕微的腦性麻痺（cerebral palsy）。小強爸爸是個食品公司全職行銷人員，媽媽則在電腦公司上班，家中有請外傭照顧小強，外傭每週一次帶小強去醫院做復健，下列何者為主要的護理措施？",50,106,{"webId":59,"stem":60,"number":41,"year":61,"session":26},"nurse-107-2-maternal-pediatric-004","潛伏期待產婦最可能有的行為反應為何？",107,"2026-09-04",1788510743032]