[{"data":1,"prerenderedAt":63},["ShallowReactive",2],{"q-nurse-111-2-maternal-pediatric-055":3},{"subject":4,"subjectSlug":5,"subjectFullName":4,"question":6,"related":33,"lastmod":62},"產兒科護理學","maternal-pediatric",{"id":7,"webId":8,"year":9,"session":10,"subject":4,"number":11,"stem":12,"options":13,"answer":18,"answerNote":19,"images":20,"explanation":21,"explanationDeep":22,"topics":23,"freq":26},"nurse-111-2-產兒科護理學-055","nurse-111-2-maternal-pediatric-055",111,2,55,"對於高胱胺酸尿症（homocystinuria, HCU）兒童的長期照護，下列何者錯誤？",{"A":14,"B":15,"C":16,"D":17},"禁食母奶，採用豆類配方之特殊奶粉（如 3200-K）","對於維生素 B6 反應不佳的兒童，需限制含甲硫胺酸食物","建議按時接受體格與智力發育評估","早期發現早期治療可以避免近視、水晶體脫垂等眼睛病變","D",null,[],"本題考點為高胱胺酸尿症(HCU)的長期照護,答案選錯誤者。考點在於眼睛病變的可逆性。HCU 為甲硫胺酸代謝異常導致同半胱胺酸堆積,雖早期治療可延緩併發症,但其典型眼部病變為「水晶體脫垂」與近視,早期發現治療可「降低或延緩」風險,惟 D 敘述以「避免」為絕對化用語且與臨床實際不符,故列為錯誤。A 需禁食母奶改用低甲硫胺酸的特殊配方(如 3200-K),正確;B 對維生素 B6 反應不佳者需限制含甲硫胺酸食物,正確;C 建議定期接受體格與智力發育評估,正確。故錯誤者為 D。","HCU 屬體染色體隱性遺傳,缺 cystathionine β-synthase,致同半胱胺酸與甲硫胺酸堆積,影響結締組織、血管與神經。臨床四大表現:水晶體脫垂(向下)、骨骼類馬凡氏症、智能障礙、血栓栓塞。治療含低甲硫胺酸飲食、補充維生素 B6(部分反應型)、甜菜鹼與葉酸。與 PKU 同屬胺基酸代謝異常需飲食控制。",[24,27,29,31],{"term":25,"count":26},"高胱胺酸尿症",1,{"term":28,"count":26},"甲硫胺酸限制",{"term":30,"count":26},"水晶體脫垂",{"term":32,"count":26},"胺基酸代謝異常",[34,38,43,48,53,58],{"webId":35,"stem":36,"number":37,"year":9,"session":10},"nurse-111-2-maternal-pediatric-056","小文，2 歲 6 個月，罹患慢性病長達一年，下列有關其壓力反應之敘述，何者最適當？",56,{"webId":39,"stem":40,"number":41,"year":42,"session":26},"nurse-112-1-maternal-pediatric-072","有關第 1 型糖尿病（Type 1 diabetes）之敘述，下列何者正確？①主要是因為自體免疫反應，使產生胰島素的 β 細胞受到破壞 ②使用口服降血糖藥物就能治療疾病 ③疾病治療的準則中，血糖監測、藥物、飲食和運動缺一不可 ④好發族群為肥胖之青少年",72,112,{"webId":44,"stem":45,"number":46,"year":42,"session":47},"nurse-112-3-maternal-pediatric-006","素食者在懷孕期較易缺乏下列何項維生素？",6,3,{"webId":49,"stem":50,"number":51,"year":52,"session":26},"nurse-114-1-maternal-pediatric-004","懷孕32週婦女，當有人經過其身旁時，會不由自主用雙手護住肚子，下列何者最能形容其孕期的母性任務行為？",4,114,{"webId":54,"stem":55,"number":56,"year":57,"session":10},"nurse-115-2-maternal-pediatric-008","影響分娩的因素中，包含母體骨盆及胎頭徑線。下列敘述何者錯誤？",8,115,{"webId":59,"stem":60,"number":41,"year":61,"session":10},"nurse-106-2-maternal-pediatric-072","罹患胰島素依賴型糖尿病（IDDM）的 12 歲病童，參加營養衛教課，當病童能說出下列何者，表示護理師此次衛教已經成功？",106,"2026-09-04",1788510739469]