[{"data":1,"prerenderedAt":64},["ShallowReactive",2],{"q-nurse-111-1-maternal-pediatric-006":3},{"subject":4,"subjectSlug":5,"subjectFullName":4,"question":6,"related":34,"lastmod":63},"產兒科護理學","maternal-pediatric",{"id":7,"webId":8,"year":9,"session":10,"subject":4,"number":11,"stem":12,"options":13,"answer":18,"answerNote":19,"images":20,"explanation":21,"explanationDeep":22,"topics":23,"freq":10},"nurse-111-1-產兒科護理學-006","nurse-111-1-maternal-pediatric-006",111,1,6,"羅女士，因 16 歲的女兒月經遲遲未來，經醫師診斷為透納式症候群（Turner syndrome），有關透納式症候群之敘述，下列何者正確？",{"A":14,"B":15,"C":16,"D":17},"其造成原因與目前塑化劑及環境荷爾蒙有關","通常會有身材矮小、第二性徵發育不全與無法生育的問題","會有月經不規則及智能遲緩的相關處置","其典型症狀為小頭、手指粗短與蹼狀足","B",null,[],"本題考點在於透納氏症候群(Turner syndrome)的臨床特徵。依其染色體核型為 45,X(缺少一條 X 染色體),患者卵巢發育不全,故典型表現為身材矮小、第二性徵發育不全(原發性無月經)與不孕,故 B 正確,為本題答案。A 病因為染色體數目異常,與塑化劑或環境荷爾蒙無關,錯誤。C 透納氏症候群患者智能多在正常範圍,並非以智能遲緩為特徵,錯誤。D 典型體徵是頸部蹼狀頸(webbed neck)、盾狀胸與手腳淋巴水腫,「小頭、手指粗短、蹼狀足」的描述不符,錯誤。","透納氏症候群核型 45,X,只影響女性,核心是卵巢功能不全→雌激素缺乏→矮小、青春期不發育、原發性無月經、不孕。特徵體徵:蹼狀頸、後髮際低、盾狀胸乳距寬、肘外翻,並常合併主動脈窄縮與腎臟異常。治療以生長激素改善身高、雌激素誘導第二性徵。對比唐氏症(21 三體)才有智能遲緩與特殊面容,兩者勿混淆。",[24,26,28,30,32],{"term":25,"count":10},"透納氏症候群",{"term":27,"count":10},"45,X 核型",{"term":29,"count":10},"卵巢發育不全",{"term":31,"count":10},"身材矮小",{"term":33,"count":10},"原發性無月經",[35,39,44,49,54,59],{"webId":36,"stem":37,"number":38,"year":9,"session":10},"nurse-111-1-maternal-pediatric-007","有關妊娠期婦女需增加熱量攝取之敘述，下列何者正確？",7,{"webId":40,"stem":41,"number":42,"year":9,"session":43},"nurse-111-2-maternal-pediatric-023","有關各種避孕方法作用原理的敘述，下列何者正確？",23,2,{"webId":45,"stem":46,"number":47,"year":48,"session":10},"nurse-112-1-maternal-pediatric-037","有關絨毛膜癌的敘述，下列何者錯誤？",37,112,{"webId":50,"stem":51,"number":52,"year":53,"session":10},"nurse-113-1-maternal-pediatric-025","王女士罹患梅毒，王女士表示先生如果知道了，他會失去先生，不停掩面哭泣，下列護理措施何者最適當？",25,113,{"webId":55,"stem":56,"number":57,"year":58,"session":43},"nurse-114-2-maternal-pediatric-029","醫護人員為未滿 1 歲兒童執行心肺復甦術，下列敘述何者錯誤？",29,114,{"webId":60,"stem":61,"number":42,"year":62,"session":10},"nurse-106-1-maternal-pediatric-023","黃女士，G 1 P 1 ，陰道生產，想在寶寶 1 歲前離奶（斷奶），下列何者錯誤？",106,"2026-09-04",1788510735364]