[{"data":1,"prerenderedAt":66},["ShallowReactive",2],{"q-nurse-110-2-basic-medicine-047":3},{"subject":4,"subjectSlug":5,"subjectFullName":6,"question":7,"related":34,"lastmod":65},"基礎醫學","basic-medicine","基礎醫學(包括解剖學、生理學、病理學、藥理學、微生物學與免疫學)",{"id":8,"webId":9,"year":10,"session":11,"subject":4,"number":12,"stem":13,"options":14,"answer":19,"answerNote":20,"images":21,"explanation":22,"explanationDeep":23,"topics":24,"freq":11},"nurse-110-2-基礎醫學-047","nurse-110-2-basic-medicine-047",110,2,47,"關於腎臟囊腫疾病（cystic disease of the kidney），下列何者錯誤？",{"A":15,"B":16,"C":17,"D":18},"單純性囊腫（simple cyst）一般為臨床上無害的變異","成人多囊性腎病（adult polycystic kidney disease）典型為雙側腎臟囊腫，且伴隨肝臟囊腫","兒童多囊性腎病（childhood polycystic kidney disease）遺傳上多為體染色體顯性（autosomal dominant）","成人多囊性腎病有許多病例與 PKD1 基因缺陷有關","C",null,[],"本題考點在腎臟囊腫疾病的遺傳與病理特徵,要求找出錯誤敘述。兒童型多囊性腎病(childhood\u002FARPKD)遺傳方式為體染色體『隱性』(autosomal recessive),而非選項C所述的顯性,故C錯誤、為答案。A正確,單純性囊腫多為偶見、臨床無害的良性變異;B正確,成人型多囊性腎病典型為雙側腎臟多發囊腫並常伴肝囊腫;D正確,成人型多與PKD1(及PKD2)基因缺陷有關。故錯誤者為兒童型的遺傳方式。","多囊腎:ADPKD(成人型,顯性,PKD1\u002FPKD2,雙側大囊腎加肝囊腫、腦動脈瘤、二尖瓣脫垂,中年發病進展至末期腎病);ARPKD(嬰兒\u002F兒童型,隱性,PKHD1,雙側集尿管擴張加先天性肝纖維化,新生兒可致Potter序列)。單純囊腫隨年齡常見、良性。可連結後天性囊腫(長期洗腎)與von Hippel-Lindau相關腎囊腫及腎細胞癌。",[25,27,30,32],{"term":26,"count":11},"體染色體隱性",{"term":28,"count":29},"兒童多囊性腎病",1,{"term":31,"count":29},"成人多囊性腎病",{"term":33,"count":29},"PKD1基因",[35,39,44,49,54,60],{"webId":36,"stem":37,"number":38,"year":10,"session":11},"nurse-110-2-basic-medicine-048","下列那一種關節炎是好發於年輕男性的薦腸骨關節及 HLA-B27 呈陽性？",48,{"webId":40,"stem":41,"number":42,"year":43,"session":29},"nurse-111-1-basic-medicine-064","當前往瘧疾疫區旅行，得知該區疫情已經對 chloroquine 產生抗藥性時，下列何者為最佳預防用藥？",64,111,{"webId":45,"stem":46,"number":47,"year":48,"session":29},"nurse-112-1-basic-medicine-028","兒童之後天性心臟病最常見者為下列那一種？",28,112,{"webId":50,"stem":51,"number":52,"year":53,"session":11},"nurse-113-2-basic-medicine-026","下列造成血小板減少的原因中，何者最可能發現骨髓的巨核細胞（megakaryocyte）減少？",26,113,{"webId":55,"stem":56,"number":57,"year":58,"session":59},"nurse-114-3-basic-medicine-030","下列何種疾病是因為 FGFR3 基因突變而造成侏儒症（dwarfism）？",30,114,3,{"webId":61,"stem":62,"number":63,"year":64,"session":29},"nurse-106-1-basic-medicine-074","病毒的構造是決定其是否能抵抗消毒劑的原因之一，下列何種病毒因不具套膜可以抵抗乙醚的破壞？",74,106,"2026-09-04",1788510727720]