[{"data":1,"prerenderedAt":67},["ShallowReactive",2],{"q-nurse-110-1-basic-medicine-044":3},{"subject":4,"subjectSlug":5,"subjectFullName":6,"question":7,"related":36,"lastmod":66},"基礎醫學","basic-medicine","基礎醫學(包括解剖學、生理學、病理學、藥理學、微生物學與免疫學)",{"id":8,"webId":9,"year":10,"session":11,"subject":4,"number":12,"stem":13,"options":14,"answer":19,"answerNote":20,"images":21,"explanation":22,"explanationDeep":23,"topics":24,"freq":27},"nurse-110-1-基礎醫學-044","nurse-110-1-basic-medicine-044",110,1,44,"下列何者不是威爾森氏病（Wilson disease）的特徵？",{"A":15,"B":16,"C":17,"D":18},"為體染色體顯性遺傳（autosomal dominant inheritance）疾病","銅離子無法被代謝，沉積在肝、腦等器官","眼睛角膜周圍可見棕綠色環","可能有神經及精神症狀","A",null,[],"本題考點是威爾森氏病的遺傳模式與特徵。依此病的遺傳學,威爾森氏病是 ATP7B 基因缺陷所致的「體染色體隱性」遺傳病,而非顯性,故問「不是其特徵」者選 A。考點在於掌握銅代謝異常的全貌:B 正確,銅無法經膽汁排出而沉積於肝、腦、角膜等器官;C 正確,銅沉積角膜緣形成棕綠色的 Kayser-Fleischer 環;D 正確,基底核受損可致震顫、構音障礙等神經與精神症狀,三者皆為威爾森氏病真實特徵,唯遺傳模式敘述有誤。","威爾森氏病核心是 ATP7B 功能喪失,銅無法併入 ceruloplasmin 也無法排入膽汁,故血中 ceruloplasmin 偏低、尿銅升高、肝與腦(尤其基底核)銅堆積。治療以銅螯合劑(penicillamine、trientine)或鋅劑減少吸收。記憶法:年輕人同時有肝病與精神神經症狀,加上眼睛 K-F 環,即為威爾森氏病的三聯線索。",[25,28,30,32,34],{"term":26,"count":27},"體染色體隱性遺傳",3,{"term":29,"count":11},"威爾森氏病",{"term":31,"count":11},"ATP7B",{"term":33,"count":11},"Kayser-Fleischer 環",{"term":35,"count":11},"ceruloplasmin",[37,41,46,51,56,61],{"webId":38,"stem":39,"number":40,"year":10,"session":11},"nurse-110-1-basic-medicine-045","病人突然發生呼吸短促、呼吸困難。顯微鏡下可見支氣管壁的平滑肌肥大，黏膜下腺體增生，伴有炎症反應，特別是嗜酸性白血球（eosinophils）增多。上列敘述最可能是那一種病症的組織反應？",45,{"webId":42,"stem":43,"number":44,"year":10,"session":45},"nurse-110-2-basic-medicine-061","下列何種藥物可預防或減輕因使用 Aspirin 造成之消化性潰瘍？",61,2,{"webId":47,"stem":48,"number":49,"year":50,"session":11},"nurse-111-1-basic-medicine-075","下列那一種細菌與引起非典型肺炎（atypical pneumonia）較為無關？",75,111,{"webId":52,"stem":53,"number":54,"year":55,"session":27},"nurse-112-3-basic-medicine-043","下列何種過敏反應主要是由 IgE 抗體所引起？",43,112,{"webId":57,"stem":58,"number":59,"year":60,"session":11},"nurse-114-1-basic-medicine-047","有關花斑癬（Pityriasis versicolor）之敘述，下列何者正確？",47,114,{"webId":62,"stem":63,"number":64,"year":65,"session":45},"nurse-115-2-basic-medicine-041","細菌對青黴素（penicillin）產生抗藥性，其最主要的機轉為何？",41,115,"2026-09-04",1788510719518]