[{"data":1,"prerenderedAt":64},["ShallowReactive",2],{"q-nurse-108-2-maternal-pediatric-074":3},{"subject":4,"subjectSlug":5,"subjectFullName":4,"question":6,"related":33,"lastmod":63},"產兒科護理學","maternal-pediatric",{"id":7,"webId":8,"year":9,"session":10,"subject":4,"number":11,"stem":12,"options":13,"answer":18,"answerNote":19,"images":20,"explanation":21,"explanationDeep":22,"topics":23,"freq":10},"nurse-108-2-產兒科護理學-074","nurse-108-2-maternal-pediatric-074",108,2,74,"有關於先天性腎上腺素增生症（congenital adrenal hyperplasia, CAH），下列敘述何者正確？",{"A":14,"B":15,"C":16,"D":17},"是一種體染色體顯性遺傳疾病","24 小時尿液 17-ketosteroids（17-KS）會下降","夜間服用 cortisone，以維持正常皮質類固醇分泌","注意每日體重、輸入、輸出量及鈉、鉀離子之平衡","D",null,[],"本題考點為先天性腎上腺增生症（CAH）的遺傳、生化變化與照護。依病生理，CAH 因酵素缺乏使皮質醇合成受阻、常伴鹽分流失，故須密切監測每日體重、輸入輸出量及鈉、鉀離子平衡，D 正確。A 錯：CAH 為體染色體「隱性」遺傳，非顯性。B 錯：因 ACTH 代償上升、雄性素前驅物堆積，24 小時尿 17-ketosteroids（17-KS）應「上升」而非下降。C 錯：類固醇補充多在清晨給予以模擬正常皮質醇分泌節律，故正解為 D。","CAH 最常見型為 21-羥化酶缺乏，皮質醇與醛固酮不足、雄性素過量，故女嬰外生殖器男性化、鹽分流失型可致低血鈉、高血鉀與脫水危象。治療以補充糖皮質素（抑制 ACTH 過度刺激）及鹽皮質素、必要時補鈉。監測電解質與體重可及早發現腎上腺危象。記憶法：CAH「隱性遺傳、17-KS 上升、缺鹽（低鈉高鉀）、補類固醇顧電解質」。急性壓力（發燒、手術）時須增加類固醇劑量以防危象。",[24,26,29,31],{"term":25,"count":10},"21-羥化酶缺乏",{"term":27,"count":28},"先天性腎上腺增生症 CAH",1,{"term":30,"count":28},"17-ketosteroids",{"term":32,"count":28},"鈉鉀電解質平衡",[34,38,43,48,53,58],{"webId":35,"stem":36,"number":37,"year":9,"session":10},"nurse-108-2-maternal-pediatric-075","小鋼，7 歲，罹患威廉氏腫瘤（Wilms tumor）第三期，即將接受腎臟切除術。下列敘述何者正確？",75,{"webId":39,"stem":40,"number":41,"year":42,"session":10},"nurse-109-2-maternal-pediatric-011","有關產婦生產用力的描述，下列何者錯誤？",11,109,{"webId":44,"stem":45,"number":46,"year":47,"session":28},"nurse-110-1-maternal-pediatric-025","陳女士產後小便尚未自解，護理師評估結果為尿瀦留，下列敘述何者正確？",25,110,{"webId":49,"stem":50,"number":51,"year":52,"session":28},"nurse-111-1-maternal-pediatric-063","陳小弟，7 個月大，因高燒、聲音出現狗吠聲而入院，經醫師診斷為哮吼（croup），有關哮吼的護理措施，下列敘述何者錯誤？",63,111,{"webId":54,"stem":55,"number":56,"year":57,"session":10},"nurse-112-2-maternal-pediatric-027","有關產後正常紅惡露（Lochia Rubra）的敘述，下列何者錯誤？",27,112,{"webId":59,"stem":60,"number":61,"year":62,"session":10},"nurse-113-2-maternal-pediatric-041","下列何者為急性淋巴性白血病最有效之鑑別診斷？",41,113,"2026-09-04",1788510707435]