[{"data":1,"prerenderedAt":61},["ShallowReactive",2],{"q-nurse-108-1-maternal-pediatric-065":3},{"subject":4,"subjectSlug":5,"subjectFullName":4,"question":6,"related":32,"lastmod":60},"產兒科護理學","maternal-pediatric",{"id":7,"webId":8,"year":9,"session":10,"subject":4,"number":11,"stem":12,"options":13,"answer":18,"answerNote":19,"images":20,"explanation":21,"explanationDeep":22,"topics":23,"freq":10},"nurse-108-1-產兒科護理學-065","nurse-108-1-maternal-pediatric-065",108,1,65,"有關囊性纖維變性（Cystic Fibrosis）之敘述，下列何者錯誤？",{"A":14,"B":15,"C":16,"D":17},"此為體染色體隱性遺傳疾病，提供家庭遺傳諮詢","止咳劑及抗組織胺藥物可以協助改善呼吸道分泌物排除","醫療計畫包括胰酵素製劑、補充脂溶性維生素及鐵劑","應採取高熱量、高蛋白飲食，且攝取大量水分","B",null,[],"本題考點在囊性纖維化的疾病管理，須選出錯誤敘述。此病特徵為呼吸道分泌物黏稠難排，治療應化痰、拍痰引流，而止咳劑會抑制咳嗽排痰反射、抗組織胺使分泌物更黏稠，兩者皆不利痰液排除，故選項 B 錯誤，即為答案。選項 A 正確，本病為第 7 對染色體 CFTR 基因缺陷的體染色體隱性遺傳，宜提供遺傳諮詢。選項 C 正確，胰功能不足致脂肪吸收不良，須補充胰酵素及脂溶性維生素（A、D、E、K）。選項 D 正確，因熱量消耗大與吸收不良，應採高熱量、高蛋白飲食並攝取充足水分。","囊性纖維化的病生理：CFTR 氯離子通道功能異常，導致外分泌腺分泌物黏稠，影響肺（反覆感染）、胰（酵素阻塞、脂肪便）、汗腺（汗液氯離子升高，汗液試驗為診斷依據）。治療核心「化痰、拍痰、補酵素、補脂溶性維生素、高熱量」。止咳劑與抗組織胺是抑制排痰的禁忌用藥。可連結概念：體染色體隱性遺傳（帶因者機率）、汗液氯離子試驗、脂肪吸收不良、胎便腸阻塞。",[24,26,28,30],{"term":25,"count":10},"囊性纖維化",{"term":27,"count":10},"CFTR 基因",{"term":29,"count":10},"止咳劑抗組織胺禁忌",{"term":31,"count":10},"脂溶性維生素",[33,37,42,46,51,56],{"webId":34,"stem":35,"number":36,"year":9,"session":10},"nurse-108-1-maternal-pediatric-066","有關以家庭為中心的兒童緩和安寧醫療照護，下列何者錯誤？",66,{"webId":38,"stem":39,"number":40,"year":41,"session":10},"nurse-109-1-maternal-pediatric-002","具有伸展會陰部肌肉功用的產前運動項目，下列何者最相關？",2,109,{"webId":43,"stem":44,"number":45,"year":41,"session":40},"nurse-109-2-maternal-pediatric-016","有關胎心率的監測，下列敘述何者錯誤？",16,{"webId":47,"stem":48,"number":49,"year":50,"session":40},"nurse-110-2-maternal-pediatric-054","小衡，7 歲，因妥瑞氏症（Tourette’s disorder），在學校常出現搖頭聳肩、發出狗叫聲，導致班上同學嘲笑，下列護理措施何者不適當？",54,110,{"webId":52,"stem":53,"number":54,"year":55,"session":10},"nurse-112-1-maternal-pediatric-018","剖腹產時，為減少藥物對胎兒的副作用，宜採用何種麻醉方式？",18,112,{"webId":57,"stem":58,"number":40,"year":59,"session":10},"nurse-113-1-maternal-pediatric-002","有關妊娠期血液檢查之敘述，下列何者正確？",113,"2026-09-04",1788510710761]