[{"data":1,"prerenderedAt":64},["ShallowReactive",2],{"q-nurse-106-2-maternal-pediatric-070":3},{"subject":4,"subjectSlug":5,"subjectFullName":4,"question":6,"related":33,"lastmod":63},"產兒科護理學","maternal-pediatric",{"id":7,"webId":8,"year":9,"session":10,"subject":4,"number":11,"stem":12,"options":13,"answer":18,"answerNote":19,"images":20,"explanation":21,"explanationDeep":22,"topics":23,"freq":26},"nurse-106-2-產兒科護理學-070","nurse-106-2-maternal-pediatric-070",106,2,70,"新生兒篩檢之代謝性異常疾病，若未及時治療，下列何者較不會影響智力的發展？",{"A":14,"B":15,"C":16,"D":17},"苯酮尿症","G-6-PD 缺乏症（Glucose-6-Phosphate Dehydrogenase）","半乳糖血症","先天性甲狀腺功能低下症","B",null,[],"本題考點在新生兒篩檢代謝疾病中,何者未及時治療較不影響智力發展。苯酮尿症(A)未治療會因苯丙胺酸堆積損傷腦部致智能不足;半乳糖血症(C)未治療會致智能障礙、肝損與白內障;先天性甲狀腺功能低下(D)是可預防智能不足的最重要原因(甲狀腺素為腦部發育所需)。三者皆與智力密切相關。G-6-PD 缺乏症(B,俗稱蠶豆症)主要在接觸氧化性物質時引發急性溶血性貧血\u002F黃疸,本身不直接損害智力發展(除非嚴重新生兒黃疸未處理致核黃疸),相對而言較不影響智力,故選 B。","各症與智力關係:PKU(缺 phenylalanine hydroxylase→苯丙胺酸毒害腦)、半乳糖血症(缺酵素→半乳糖堆積傷腦肝眼)、先天甲狀腺低下(缺甲狀腺素→腦發育遲滯,即呆小症)——皆須早治防智能損傷。G-6-PD 缺乏是紅血球酵素缺陷,問題在氧化壓力下溶血(蠶豆、樟腦丸、某些藥物、感染誘發),衛教重點是『避免誘發物』,本身不損智力。記憶:『蠶豆症管的是溶血不是腦;其他三個不治都會變笨』。",[24,27,29,30],{"term":25,"count":26},"先天性甲狀腺功能低下",8,{"term":14,"count":28},4,{"term":16,"count":10},{"term":31,"count":32},"G-6-PD 缺乏症(溶血性)",1,[34,38,43,48,53,58],{"webId":35,"stem":36,"number":37,"year":9,"session":10},"nurse-106-2-maternal-pediatric-071","章小妹，出生 3 天的足月兒，疑似罹患先天性腎上腺增生症，下列敘述何者錯誤？",71,{"webId":39,"stem":40,"number":41,"year":42,"session":10},"nurse-107-2-maternal-pediatric-007","針對胎兒胚胎發育成身體各器官及構造中，下列何者是由中胚層發育而來？",7,107,{"webId":44,"stem":45,"number":46,"year":47,"session":32},"nurse-108-1-maternal-pediatric-021","李女士剖腹生產後第 1 天，生命徵象正常，尚未排氣，惡露為少量的深紅色，下列護理指導何者適當？",21,108,{"webId":49,"stem":50,"number":51,"year":52,"session":32},"nurse-109-1-maternal-pediatric-059","小英，5 個月，採心尖脈測量心跳，有關心尖脈位置之敘述，下列何者正確？",59,109,{"webId":54,"stem":55,"number":56,"year":57,"session":10},"nurse-110-2-maternal-pediatric-023","婦女於正常陰道生產後的復舊生理變化，下列何者所需時間最長？",23,110,{"webId":59,"stem":60,"number":61,"year":62,"session":10},"nurse-111-2-maternal-pediatric-057","小華，5 歲，因其 3 歲弟弟罹患慢性疾病，需反覆長期住院，下列何者較不是造成小華壓力反應的風險因子？",57,111,"2026-09-04",1788510699746]