[{"data":1,"prerenderedAt":64},["ShallowReactive",2],{"q-nurse-106-2-maternal-pediatric-067":3},{"subject":4,"subjectSlug":5,"subjectFullName":4,"question":6,"related":33,"lastmod":63},"產兒科護理學","maternal-pediatric",{"id":7,"webId":8,"year":9,"session":10,"subject":4,"number":11,"stem":12,"options":13,"answer":18,"answerNote":19,"images":20,"explanation":21,"explanationDeep":22,"topics":23,"freq":26},"nurse-106-2-產兒科護理學-067","nurse-106-2-maternal-pediatric-067",106,2,67,"小華，7 歲，罹患重度型 β-海洋性貧血，定期接受輸血治療，有關其外觀的視診結果，下列敘述何者錯誤？",{"A":14,"B":15,"C":16,"D":17},"體型矮瘦","膚色蒼白","塌鼻、頭大","腹部腫大","B",null,[],"本題考點在重度型 β-地中海型貧血(β-thalassemia major)的外觀視診特徵,採反向題。此症因慢性溶血與骨髓代償性增生,典型外觀為生長遲滯體型矮瘦(A)、骨髓擴張致顱骨與臉骨變形呈塌鼻頭大(C)、髓外造血與鐵沉積致肝脾腫大而腹部膨大(D)。B『膚色蒼白』雖貧血會蒼白,但重度地中海貧血因長期溶血與反覆輸血鐵質沉積,膚色特徵反而是『古銅色\u002F暗沉』而非單純蒼白,故此敘述作為特徵描述錯誤,選 B。核心在鐵過載使膚色偏古銅,而非蒼白。","β-地中海貧血因 β 球蛋白鏈合成不足→無效造血與溶血。骨髓代償性增生使骨骼變形:額骨隆起、顴骨突、塌鼻(chipmunk facies)、X 光顱骨呈『毛髮豎立狀(hair-on-end)』。長期輸血致含鐵血黃素沉積(hemosiderosis),皮膚呈古銅\u002F青銅色,並傷及心、肝、內分泌,故需鐵螯合治療(deferoxamine)。肝脾腫大源於髓外造血與鐵沉積。記憶:『地中海貧血=塌鼻頭大、矮瘦、肝脾大、鐵沉古銅色』;單純蒼白反而是干擾選項。",[24,27,29,31],{"term":25,"count":26},"β-地中海型貧血",1,{"term":28,"count":26},"骨髓代償增生與顏面骨變形",{"term":30,"count":26},"鐵過載(古銅色皮膚)",{"term":32,"count":26},"肝脾腫大",[34,38,43,48,53,58],{"webId":35,"stem":36,"number":37,"year":9,"session":10},"nurse-106-2-maternal-pediatric-068","有關兒童感染人類免疫缺乏病毒（HIV）的途徑，下列何者錯誤？",68,{"webId":39,"stem":40,"number":41,"year":42,"session":10},"nurse-107-2-maternal-pediatric-004","潛伏期待產婦最可能有的行為反應為何？",4,107,{"webId":44,"stem":45,"number":46,"year":47,"session":26},"nurse-108-1-maternal-pediatric-018","陳女士陰道檢查結果子宮頸擴張 9 公分，變薄程度 80%，高度+2，此時胎頭最有可能在下列那個位置？",18,108,{"webId":49,"stem":50,"number":51,"year":52,"session":26},"nurse-109-1-maternal-pediatric-056","小銘，2 歲，罹患典型的異戊酸血症（Isovaleric Acidemia），下列敘述何者正確？",56,109,{"webId":54,"stem":55,"number":56,"year":57,"session":10},"nurse-110-2-maternal-pediatric-020","李女士，哺餵母乳，產後出院前表示：「我暫時不想懷孕，想跟以前一樣吃避孕藥，可以考慮使用避孕器，其他方法就不用了。」，下列敘述何者最適當？",20,110,{"webId":59,"stem":60,"number":61,"year":62,"session":10},"nurse-111-2-maternal-pediatric-054","早產兒若氧氣濃度超過 60%，PaO 2 \u003C 60 mmHg 時，醫囑使用持續性氣道正壓呼吸（CPAP），下列敘述何者不適當？",54,111,"2026-09-04",1788510699721]