[{"data":1,"prerenderedAt":65},["ShallowReactive",2],{"q-nurse-106-1-maternal-pediatric-068":3},{"subject":4,"subjectSlug":5,"subjectFullName":4,"question":6,"related":35,"lastmod":64},"產兒科護理學","maternal-pediatric",{"id":7,"webId":8,"year":9,"session":10,"subject":4,"number":11,"stem":12,"options":13,"answer":18,"answerNote":19,"images":20,"explanation":21,"explanationDeep":22,"topics":23,"freq":26},"nurse-106-1-產兒科護理學-068","nurse-106-1-maternal-pediatric-068",106,1,68,"有關苯酮尿症（Phenylketonuria）病童飲食指導之敘述，下列何者錯誤？",{"A":14,"B":15,"C":16,"D":17},"於確定診斷後，即開始終身飲食控制","嬰幼兒時，餵食特殊配方奶 Lofenalac 和 Phenyl-Free","長大後可以多補充水果、蔬菜、根類或澱粉類食物","應限制麵粉製品、肉類、魚類、牛奶及豆類等食物","A",null,[],"本題考點為苯酮尿症的飲食治療原則。PKU因苯丙胺酸羥化酶缺乏無法代謝苯丙胺酸,治療核心是低苯丙胺酸飲食。B以Lofenalac、Phenyl-Free特殊配方奶提供低或不含苯丙胺酸的蛋白來源(對),C長大後可多補充水果、蔬菜、根莖與澱粉等低蛋白食物(對),D須限制麵粉、肉、魚、牛奶與豆類等高蛋白高苯丙胺酸食物(對)。A為錯誤:飲食控制應在新生兒篩檢確認後儘早於出生數週內開始,以把握腦部發育黃金期,而非等到「確定診斷後」才介入,延誤起始時機將造成不可逆的智能損傷。","苯丙胺酸堆積會產生神經毒性代謝物,傷害發育中大腦導致智能障礙與癲癇;治療愈早成效愈好,故新生兒篩檢陽性即需低苯丙胺酸配方並終身監測血中濃度(女性尚有母性PKU風險)。完全禁蛋白會缺乏必需胺基酸,故用特殊配方補足去苯丙胺酸的蛋白。本題A之爭點在起始時機的用詞,對出題原意保留,故標記medium。",[24,27,30,33],{"term":25,"count":26},"新生兒篩檢",13,{"term":28,"count":29},"苯酮尿症",4,{"term":31,"count":32},"低苯丙胺酸飲食",2,{"term":34,"count":10},"苯丙胺酸羥化酶",[36,40,45,49,54,59],{"webId":37,"stem":38,"number":39,"year":9,"session":10},"nurse-106-1-maternal-pediatric-069","小樺，7 歲，最近因持續發燒、易流鼻血而求診，診斷疑似急性淋巴性白血病，下列那一項檢查結果可以確定其診斷？",69,{"webId":41,"stem":42,"number":43,"year":44,"session":10},"nurse-107-1-maternal-pediatric-005","王女士，孕前 BMI 值為 24，目前懷孕 25 週，體重較孕前增加 3 公斤，有關護理師的回應，下列何者較為適當？",5,107,{"webId":46,"stem":47,"number":48,"year":44,"session":32},"nurse-107-2-maternal-pediatric-019","當待產婦使用 PGE 2 陰道栓劑後，護理師需要監測下列何種變化？",19,{"webId":50,"stem":51,"number":52,"year":53,"session":32},"nurse-108-2-maternal-pediatric-057","小英，4 歲，因中耳炎需執行耳內給藥，給藥時，應將小英耳朵往那一方向拉？",57,108,{"webId":55,"stem":56,"number":57,"year":58,"session":10},"nurse-110-1-maternal-pediatric-021","下列何者為更年期女性的生理變化？①濾泡刺激素大量增加 ②雌性素分泌增加 ③低密度脂蛋白增加 ④陰道 pH 值下降",21,110,{"webId":60,"stem":61,"number":62,"year":63,"session":10},"nurse-111-1-maternal-pediatric-055","有關新生兒胎便吸入症候群的敘述，下列何者錯誤？",55,111,"2026-09-04",1788510694346]